CI

At a glance

ClinicalIndex Comparison Record
Phase 1Recruiting· 56 target
Drug / intervention
DNAJB1-PRKACA peptide vaccine +2 moredrug
Likely dose
DNAJB1-PRKACA peptide vaccine 0.3 mgfrom record
Key inclusion· 11
  • Histologically confirmed fibrolamellar hepatocellular cancer (FLC) that is metastatic or unresectable
  • DNAJB1-PRKACA fusion transcript positive confirmed by RNA-sequencing, DNA-sequencing, or in situ hybridization
  • Age >12 years for Cohorts A and B; ≥18 years for Cohort C
  • Body weight ≥40 kg for patients <18 years old in Cohorts A and B
Key exclusion· 23
  • Prior treatment with checkpoint inhibitors (anti-PD-1, anti-PD-L1, anti-PD-L2, anti-CD137, anti-OX-40, anti-CD40, anti-CTLA-4, anti-LAG-3) for Cohorts A and C
  • Prior unacceptable, life-threatening toxicity from immune therapy (Cohort B)
  • Chemotherapy, biological therapy, or radiation within 14 days prior to first dose
  • Surgery within 28 days of dosing, excluding minor procedures

Standardized by ClinicalIndex from the ClinicalTrials.gov record · verify against the source.

Search/NCT04248569
NCT04248569Phase 1RecruitingOn TrackUpdated 6mo ago
Long Recruiting

A Pilot Study of a DNAJB1-PRKACA Fusion Kinase Peptide Vaccine Combined With Nivolumab and Ipilimumab for Patients With Fibrolamellar Hepatocellular Carcinoma

Sidney Kimmel Comprehensive Cancer Center at Johns Hopkins·interventional·Posted Jan 30, 2020·Updated Dec 3, 2025

In Brief

A Phase 1 clinical trial evaluating DNAJB1-PRKACA peptide vaccine, Nivolumab, and 1 other intervention for Fibrolamellar Hepatocellular Carcinoma (FLC). Currently recruiting, targeting 56 participants across 1 site.

Detailed Summary

The primary objective of the trial is the safety and tolerability of administering a vaccine targeting the DNAJB1-PRKACA fusion kinase, in combination with nivolumab and ipilimumab in patients with unresectable or metastatic FLC and with non-FLC solid tumors and to assess the T-cell response.

Study Details

Study Typeinterventional
Allocation--
Masking--
Primary Purpose--
CountriesUnited States

Timeline

Phase 1Recruiting
202020212022202320242025202620272028202920302031203220332034
First PostedJan 30, 2020
Enrollment StartApr 20, 2020
Primary CompletionMar 1, 2029
Study CompletionMar 1, 2034
TodayJul 2, 2026
Enrollment to primary: 8.9 yearsPosted 6.4 years agoPrimary completion in 2.7 years

Interventions

DNAJB1-PRKACA peptide vaccinedrug

1. DNAJB1-PRKACA peptide vaccine: Day 1, 8, 15 of cycle 1 and on Day 1 of cycle 2, 3 and 4 (priming phase). Boost vaccinations: every 3 cycles beginning C5D1. 2. Drug: 0.3 mg DNAJB1-PRKACA peptide vaccine + 0.5mg Poly-ICLC

Nivolumabdrug

1. Nivolumab 3mg/kg will be administered as a 30 minute IV infusion (-10/+15min) on Day 1 of Cycle 1-4 during the priming phase. Boost/maintenance vaccinations will be administered as a flat dose of 480mg every 4 weeks starting on Day 1 of Cycle 5. 2. Drug: 3mg/kg and 480mg IV

Ipilimumabdrug

1. Ipilimumab (1 mg/kg) will be administered as a 30 minute IV infusion (-10/+15min) on Day 1 of Cycles 1, 2, 3 and 4 of the study, every 3 weeks of the priming phase. 2. Drug: 1mg/kg IV